Diffuse Caroli's disease with atypical presentation: a case report

Abstract

This paper describes a case of Caroli's disease in a female patient aged 32, who complained of nonspecific abdominal pain without cholesthasis or cholangitis. Liver resonance shows segment saccular dilations closely connected to intrahepatic biliary ducts, that differ from the Caroli's syndrome, which is more common and consists of multiple intrahepatic cystic dilatations, associated to congenital hepatic fibrosis. This patient has a congenital anomaly with an uncommon oligosymptomatic form of Caroli's disease that should be included in the differential diagnosis of patients with recurrent abdominal pain.

Keywords Cholangiopathy, Caroli's syndrome, Von Meyenburg complex, congenital bile duct dilatation

Ann Gastroenterol 2014; 27 (1): 79-81